Cleidocranial Dysostosis – An Enigma Developmental Bones Anomaly

Cleidocranial Dysostosis, known also as Cleidocranial dysplasia, Mutational Dysostosis, Scheuthauer Marie-Sainton syndrome, is a rare condition which is characterized by delayed ossification of midline structures. Case study of the phenomenon has been reported here. Reports revealed that the classical association of a spectacular dental anarchy, with non-closure of cranial sutures, retention of deciduous teeth and delayed eruption of permanent denture and typical facies of underdevelopment raise strong suspicion of autosomal syndrome. The reviewed patient as a classic demonstration of cleidocranial dysostosis, succinctly represented the condition.