Recurrent Dermatofibrosarcoma Protuberans of Head and Neck: A Rare Case Report

Dermatofibrosarcoma protuberans (DFSP) is an uncommon neoplasm of dermis involving head neck region. This tumour is slow growing and has very high potential for local recurrence with less risk of metastasis. It is a very rare neoplasm of the dermis layer of the skin [1] and is classified as a cutaneous soft tissue sarcoma [1]. It accounts for approximately 1–2% of all soft-tissue sarcomas. About 85% to 90% of DFSPs are low-grade tumours. The remaining 10–15% exhibit a high-grade fibrosarcomatous component and are considered high-grade lesions associated with a higher risk of metastasis [2]. We report a case of 46 years old male patient who presented with third episode of DFSP. The first episode was on right side of fore head, the second one was on right frontoparietal region and latest lesion was on right preauricular region and right pinna. On all the three occasions the recurrence was away from primary site.